A homozygous SFTPA1 mutation drives necroptosis of typeⅡ alveolar epithelial cells in patients with idiopathic pulmonary fibrosis

• Material Type: 博士論文
• Title: A homozygous SFTPA1 mutation drives necroptosis of typeⅡ alveolar epithelial cells in patients with idiopathic pulmonary fibrosis
• Author/Editor: 竹﨑, 彰夫; 九十九, 伸一; セトグチ, ヤスヒロ; Ledford, Julie G.; 後東, 久嗣; ホソミチ, カズヨシ; 上原, 久典; 西岡, 安彦; 安友, 康二
• Author Heading: 竹﨑, 彰夫 タケザキ, アキオ; 九十九, 伸一; セトグチ, ヤスヒロ セトグチ, ヤスヒロ; Ledford, Julie G.; 後東, 久嗣; ホソミチ, カズヨシ ホソミチ, カズヨシ; 上原, 久典; 西岡, 安彦; 安友, 康二
• Publication, Distribution, etc.: Rockefeller University Press
• Publication Date: 2019-10-10
• Publication Date (W3CDTF): 2019-10-10
• Alternative Title: ホモ接合型SFTPA1変異により特発性肺線維症患者のⅡ型肺胞上皮細胞のnecroptosisが亢進する; A mutation in SFTPA1 and pulmonary fibrosis
• Periodical title: Journal of Experimental Medicine
• No. or year of volume/issue: 216 12
• Volume: 216
• Issue: 12
• Pages: 2724-2735
• ISSN (Periodical Title): ISSN : 15409538; ISSN : 00221007
• Dissertation Number: 甲医第1457号
• Text Language Code: und
• Subject Heading: idiopathic pulmonary fibrosis; SFTPA1 mutation; typeⅡ alveolar epithelial cell; necroptosis
• Target Audience: 一般
• Format (IMT): application/pdf
• Source: fulltext; https://tokushima-u.repo.nii.ac.jp/record/2007627/files/k3426_fulltext.pdf
• Access Restrictions: インターネット公開
• Rights (production): © 2019 Takezaki et al. This article is distributed under the terms of an Attribution–Noncommercial–Share Alike–No Mirror Sites license for the first six months after the publication date (see http://www.rupress.org/terms/). After six months it is available under a Creative Commons License (Attribution–Noncommercial–Share Alike 4.0 International license, as described at https://creativecommons.org/licenses/by-nc-sa/4.0/).
• Periodical Title (NCID): AA12119243; https://ci.nii.ac.jp/ncid/AA12119243; AA00697559; https://ci.nii.ac.jp/ncid/AA00697559
• Data Provider (Database): 国立情報学研究所 : 学術機関リポジトリデータベース（IRDB）（機関リポジトリ）; https://irdb.nii.ac.jp
• Original Data Provider (Database): 徳島大学 : 徳島大学機関リポジトリ

• Summary, etc.: Idiopathic pulmonary fibrosis (IPF) is a fatal disease characterized by scattered fibrotic lesions in the lungs. The pathogenesis and genetic basis of...